Recurrent Priapism in Adolescent with Sickle Cell Anemia: What to do?

Author(s): Ligia Yumi Suzuki Moitinho, Livia Fratelli, Livia Tomita Goncalves, Gabriel de Azambuja Beigin, Luis Cesar Fava Spessoto, Fernando Nestor Facio Junior

In this report, we present a case of an adolescent with sickle cell anemia and a history of recurring ischemic priapism. Thirty-two hours after the onset of priapism, the patient was submitted to drainage, washing with an adrenaline solution, local ice, a non-steroidal anti-inflammatory drug and tadalafil (5 mg/day). However, However, tumescence remained and corpus cavernosum-corpus spongiosum shunt was performed. Such patients should be treated at a specialized medical center to avoid complications, such as diminished erectile function and dissatisfaction with one’s sex life in the future. Although the early implantation of a penile prosthesis can avoid further episodes of priapism, there is no consensus in the literature on the indication of a penile implant for individuals less than 18 years of age.

Priapism, Ischemic Priapism, Sickle Cell Anemia, Penile Prosthesis, Corpus Cavernosum-Corpus Spongiosum Shunt

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